Congenital pulmonary lymphangiectasia

Elizabeth Doecke

    Research output: Contribution to journalArticlepeer-review

    2 Citations (Scopus)


    Congenital pulmonary lymphangiectasia is a rare condition caused by failure of pulmonary lymphatic vessels to develop normally. It is a known cause of non-immune hydops fetalis and congenital chylothorax. While it has been recognised in the literature since the 1950s, no standardised treatment has yet emerged and a definitive cause is still unknown. This review seeks to draw together current information on diagnosis, treatment and prognosis, and to recommend that a systemic evaluation of such would provide direction for clinicians in dealing with patients affected by this condition.

    Original languageEnglish
    Pages (from-to)30-35
    Number of pages6
    JournalJournal of Lymphoedema
    Issue number2
    Publication statusPublished - 2014


    • Chylothorax
    • Congenital pulmonary lymphangiectasia
    • Foetal lymphatic development
    • Non-immune hydrops fetalis
    • Pulmonary lymphatics


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