Abstract
Congenital pulmonary lymphangiectasia is a rare condition caused by failure of pulmonary lymphatic vessels to develop normally. It is a known cause of non-immune hydops fetalis and congenital chylothorax. While it has been recognised in the literature since the 1950s, no standardised treatment has yet emerged and a definitive cause is still unknown. This review seeks to draw together current information on diagnosis, treatment and prognosis, and to recommend that a systemic evaluation of such would provide direction for clinicians in dealing with patients affected by this condition.
| Original language | English |
|---|---|
| Pages (from-to) | 30-35 |
| Number of pages | 6 |
| Journal | Journal of Lymphoedema |
| Volume | 9 |
| Issue number | 2 |
| Publication status | Published - 2014 |
Keywords
- Chylothorax
- Congenital pulmonary lymphangiectasia
- Foetal lymphatic development
- Non-immune hydrops fetalis
- Pulmonary lymphatics